Bilimsel çalışmalar

Doç. Dr. Almala Pınar Ergenekon

175 yayın. Her yayının yanında bilginin kaynağı yazar.

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  1. Evaluation of Pulmonary and Otological Manifestations in Primary Ciliary Dyskinesia and Their Effect on Quality of Life

    Pediatric pulmonology, 2026

    DOI 10.1002/ppul.71810 PMID 42643099 Açık erişimli tam metinKaynak: Europe PMC

  2. Clinical Characteristics and Treatment Outcomes After First <i>Achromobacter</i> Isolation in Children with Cystic Fibrosis (Pre-CFTR Modulator Era)

    Thoracic research and practice, 2026

    DOI 10.4274/thoracrespract.2026.2026-1-8 PMID 42642966 Açık erişimli tam metinKaynak: Europe PMC

  3. Evaluation of Pulmonary Complications in Patients with Esophageal Atresia

    European Respiratory Journal, 2026

    DOI 10.1183/13993003.congress-2026.pa1733 Kaynak: OpenAlex

  4. Long-term pulmonary function outcomes in patients with primary ciliary dyskinesia

    European Respiratory Journal, 2026

    DOI 10.1183/13993003.congress-2026.pa1728 Kaynak: OpenAlex

  5. Impact of CFTR Modulator Therapy on Muscle Strength in Pediatric Cystic Fibrosis Patients

    European Respiratory Journal, 2026

    DOI 10.1183/13993003.congress-2026.pa3958 Kaynak: OpenAlex

  6. Prolonged neonatal jaundice in infants with cystic fibrosis: a retrospective Cohort study

    European Respiratory Journal, 2026

    DOI 10.1183/13993003.congress-2026.pa3960 Kaynak: OpenAlex

  7. Evaluation of lung function via spirometry and impulse oscillometry in preschool children with wheezing

    European Respiratory Journal, 2026

    DOI 10.1183/13993003.congress-2026.pa2756 Kaynak: OpenAlex

  8. Bone mineral density in children and adolescents with cystic fibrosis: a cross-sectional study

    European Respiratory Journal, 2026

    DOI 10.1183/13993003.congress-2026.pa3947 Kaynak: OpenAlex

  9. Vaccination Status and Attitudes in Patients with Cystic Fibrosis

    European Respiratory Journal, 2026

    DOI 10.1183/13993003.congress-2026.oa2373 Kaynak: OpenAlex

  10. Knowledge Level of Home Healthcare Personnel on Cystic Fibrosis: Evaluation Before and After Training

    European Respiratory Journal, 2026

    DOI 10.1183/13993003.congress-2026.pa3949 Kaynak: OpenAlex

  11. Effective Pseudomonas aeruginosa Eradication in Cystic Fibrosis: Multicenter Study

    Clinical Pediatrics, 2025

    DOI 10.1177/00099228251351699 PMID 40576045 1 atıf (Europe PMC) Kaynak: OpenAlex

  12. National Registry for Home Mechanical Ventilation in Children from Turkey

    Respiration, 2025

    DOI 10.1159/000543343 PMID 39809249 2 atıf (Europe PMC) Açık erişimli tam metinKaynak: OpenAlex

  13. Long-term Home Mechanical Ventilation of Children in İstanbul

    Thoracic research and practice, 2025

    DOI 10.4274/thoracrespract.2024.24042 PMID 39930731 1 atıf (Europe PMC) Açık erişimli tam metinKaynak: OpenAlex

  14. Eradication of Methicillin-Resistant Staphylococcus aureus in Cystic Fibrosis

    Clinical Pediatrics, 2025

    DOI 10.1177/00099228251375413 PMID 41035301 Kaynak: OpenAlex

  15. Comparison of interrupted and continuous modulator therapy in cystic fibrosis: a real life experience in Turkey

    Frontiers in Pediatrics, 2025

    DOI 10.3389/fped.2025.1659633 PMID 41158800 1 atıf (Europe PMC) Açık erişimli tam metinKaynak: OpenAlex

  16. Increasing Cystic Fibrosis Knowledge of Parents of Children Diagnosed With the Newborn Screening Program

    Pediatric Pulmonology, 2025

    DOI 10.1002/ppul.71392 PMID 41255258 Açık erişimli tam metinKaynak: OpenAlex

  17. Current practices and variations in pediatric flexible bronchoscopy: First national survey of pediatric pulmonologists in Türkiye

    European Respiratory Journal, 2025

    DOI 10.1183/13993003.congress-2025.pa3108 Kaynak: OpenAlex

  18. Personalized Management and Timing of Thymectomy in Juvenile Myasthenia Gravis: Insights from Routine Clinical Scale Use in a Single-Center Retrospective Cohort—A Case Series

    Children, 2025

    DOI 10.3390/children12101389 PMID 41153571 Açık erişimli tam metinKaynak: OpenAlex

  19. The Coronal and Sagittal Vertebral Balance is Affected by the Severity of the Disease in Pediatric Patients with Cystic Fibrosis: A Pulmonary Function Test-Based Cross-Sectional Study

    Journal of Pediatric Orthopaedics, 2025

    DOI 10.1097/bpo.0000000000002947 PMID 40045563 Kaynak: OpenAlex

  20. Feeding the Need: A Study on Food Security Among People With Cystic Fibrosis in Turkey

    Pediatric pulmonology, 2025

    DOI 10.1002/ppul.71101 PMID 40325925 1 atıf (Europe PMC) Açık erişimli tam metinKaynak: Europe PMC

  21. Elexacaftor/Tezacaftor/Ivacaftor Treatment Accessibility and Mental Health: Reducing Anxiety in People With Cystic Fibrosis

    Pediatric pulmonology, 2025

    DOI 10.1002/ppul.71037 PMID 40062574 5 atıf (Europe PMC) Açık erişimli tam metinKaynak: Europe PMC

  22. Implementation of Cystic Fibrosis Responsibility, Independence, Self-Care, Education Program Enhances Cystic Fibrosis Knowledge in Limited Resource Country: Results From a Randomized Controlled Trial

    Pediatric pulmonology, 2025

    DOI 10.1002/ppul.27506 PMID 39898696 3 atıf (Europe PMC) Açık erişimli tam metinKaynak: Europe PMC

  23. Pulmonary function in children post-empyema: spirometry <i>versus</i> lung clearance index

    ERJ open research, 2025

    DOI 10.1183/23120541.00855-2024 PMID 40874169 Açık erişimli tam metinKaynak: Europe PMC

  24. Empowering limited-resource countries: collaborating with expert centers for diagnosis of primary ciliary dyskinesia

    Frontiers in Molecular Biosciences, 2025

    DOI 10.3389/fmolb.2025.1547152 PMID 40182617 5 atıf (OpenAlex) Açık erişimli tam metinKaynak: OpenAlex

  25. Retrospective analysis of sleep-disordered breathing in pediatric neuromuscular disease

    Trends in Pediatrics, 2025

    DOI 10.59213/tp.2025.209 1 atıf (OpenAlex) Açık erişimli tam metinKaynak: OpenAlex

  26. Clinical and demographic characteristics of patients diagnosed with Primary Ciliary Dyskinesia with CCDC40 homozygous mutation

    European Respiratory Journal, 2025

    DOI 10.1183/13993003.congress-2025.pa5919 Kaynak: OpenAlex

  27. Cystic Fibrosis Treatment Landscape: Progress, Challenges, and Future Directions

    Turkish archives of pediatrics, 2025

    DOI 10.5152/turkarchpediatr.2025.24257 PMID 40091461 3 atıf (Europe PMC) Açık erişimli tam metinKaynak: Europe PMC

  28. The Validity and Reliability of the Turkish Version of the AWESCORE Test

    Turkish archives of pediatrics, 2025

    DOI 10.5152/turkarchpediatr.2025.24199 PMID 40091631 Açık erişimli tam metinKaynak: Europe PMC

  29. Microbial Contamination of Nebulizers in Patients With Cystic Fibrosis

    Turkish Archives of Pediatrics, 2025

    DOI 10.5152/turkarchpediatr.2025.24003 PMID 39803923 2 atıf (OpenAlex) Açık erişimli tam metinKaynak: OpenAlex

  30. After the earthquake: Unmet needs in people with cystic fibrosis in Turkiye- multicenter study

    Journal of Cystic Fibrosis, 2025

    DOI 10.1016/j.jcf.2025.06.008 PMID 40675865 1 atıf (OpenAlex) Kaynak: OpenAlex

  31. A Hypomorphic Variant in Surfactant Protein B Deficiency : Survival of Two Patients

    Pediatric Pulmonology, 2025

    DOI 10.1002/ppul.71218 PMID 40709663 1 atıf (OpenAlex) Açık erişimli tam metinKaynak: OpenAlex

  32. Healthy Homes, Healthy Lungs: The Role of Home Insulation in Environmental Impact on People With Cystic Fibrosis

    Pediatric Pulmonology, 2025

    DOI 10.1002/ppul.71253 PMID 40873110 1 atıf (OpenAlex) Kaynak: OpenAlex

  33. Relation of Serum IGF-1 and IGFBP-3 Levels with Acute Exacerbation in Cystic Fibrosis

    The Journal of Pediatric Research, 2025

    DOI 10.4274/jpr.galenos.2025.88319 Açık erişimli tam metinKaynak: OpenAlex

  34. Sleep-disordered breathing in people with cystic fibrosis

    European Respiratory Journal, 2025

    DOI 10.1183/13993003.congress-2025.pa1627 Kaynak: OpenAlex

  35. The long-term impact of targeted nutritional interventions on BMI percentiles in children with cystic fibrosis.

    European Respiratory Journal, 2025

    DOI 10.1183/13993003.congress-2025.pa4801 Kaynak: OpenAlex

  36. Sleep-disordered breathing in patients with prader-willi syndrome

    European Respiratory Journal, 2025

    DOI 10.1183/13993003.congress-2025.pa2733 Kaynak: OpenAlex

  37. CFTR modulators and MRSA in real-world practice: A three-group perspective

    European Respiratory Journal, 2025

    DOI 10.1183/13993003.congress-2025.oa3326 Kaynak: OpenAlex

  38. Early Diagnosis of Sleep Disorders: Polysomnographic Findings in Children Aged 0-24 Months

    European Respiratory Journal, 2025

    DOI 10.1183/13993003.congress-2025.oa4365 Kaynak: OpenAlex

  39. Group psychotherapy for anxiety, depression, and quality of life in Cystic Fibrosis

    European Respiratory Journal, 2025

    DOI 10.1183/13993003.congress-2025.pa3987 Kaynak: OpenAlex

  40. P346 The link between fat intake and pancreatic enzyme replacement dosage with growth in children with cystic fibrosis

    Journal of Cystic Fibrosis, 2025

    DOI 10.1016/j.jcf.2025.03.1231 Kaynak: OpenAlex

  41. P316 The link between food insecurity and nutrition in children with cystic fibrosis

    Journal of Cystic Fibrosis, 2025

    DOI 10.1016/j.jcf.2025.03.1202 Kaynak: OpenAlex

  42. EPS2.08This study explores unmet needs and insecurity among people with cystic fibrosis living in earthquake-affected zones of Turkiye, conducted as a multicenter study

    Journal of Cystic Fibrosis, 2025

    DOI 10.1016/j.jcf.2025.03.605 Kaynak: OpenAlex

  43. Understanding Pulmonary Fibrosis in Pediatric Interstitial Lung Disease:A Comprehensive Analysis

    European Respiratory Journal, 2025

    DOI 10.1183/13993003.congress-2025.pa3818 Kaynak: OpenAlex

  44. Implementation of a high fidelity simulation based training program for physicians of children requiring long term invasive home ventilation: a study by ISPAT team

    Frontiers in Pediatrics, 2024

    DOI 10.3389/fped.2024.1325582 PMID 38362002 2 atıf (Europe PMC) Açık erişimli tam metinKaynak: OpenAlex

  45. The Association between Aminoglycoside Exposure and Ototoxicity in Children with Cystic Fibrosis

    Respiration, 2024

    DOI 10.1159/000541447 PMID 39299224 1 atıf (Europe PMC) Kaynak: OpenAlex

  46. NATIONAL REGISTRY SYSTEM FOR HOME MECHANICAL VENTILATION SUPPORT IN CHILDREN: FIRST DATA FROM TURKEY

    European Respiratory Journal, 2024

    DOI 10.1183/13993003.congress-2024.oa4656 Kaynak: OpenAlex

  47. Unveiling the Respiratory Muscle Strength in Duchenne Muscular Dystrophy: The Impact of Nutrition and Thoracic Deformities, Beyond Spirometry

    Children, 2024

    DOI 10.3390/children11080994 PMID 39201929 Açık erişimli tam metinKaynak: OpenAlex

  48. Is the Pediatric Sleep Questionnaire sensitive for sleep-disordered breathing in children with complex chronic disease?

    Sleep & breathing = Schlaf & Atmung, 2024

    DOI 10.1007/s11325-023-02915-z PMID 37733254 12 atıf (Europe PMC) Açık erişimli tam metinKaynak: Europe PMC

  49. Exploring Turkey's mosaic of novel variants and complex alleles in cystic fibrosis genetics

    Pediatric pulmonology, 2024

    DOI 10.1002/ppul.27249 PMID 39291770 5 atıf (Europe PMC) Açık erişimli tam metinKaynak: Europe PMC

  50. Beyond the 10%: Unraveling the genetic diversity in Turkish cystic fibrosis patients not eligible for CFTR modulators

    Pediatric pulmonology, 2024

    DOI 10.1002/ppul.27181 PMID 39031495 4 atıf (Europe PMC) Açık erişimli tam metinKaynak: Europe PMC